The full Klüver-Bucy syndrome (KBS) – hyperorality, placidity, hypermetamorphosis, dietary changes, altered sexual behavior, and visual. Klüver-Bucy syndrome is a very rare cerebral neurological disorder associated with damage to both temporal lobes resulting in abnormalities in memory, social . Klüver-Bucy syndrome is described here because its cause is usually bilateral lesions in the territory of the PCAs. In the small number of reports of the syndrome .

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Rare Disease Database

Affected individuals become increasingly forgetful. Goscinski I, et al. Alone we are rare. Major symptoms may include excessive oral tendencies with an urge to put all kinds of objects zyndrome the mouth, hypermetamorophosis a need to explore everythingmemory loss, emotional changes, extreme sexual behavior, indifference, placidity, visual distractibility and visual agnosia difficulty identifying and processing visual information.

The content of the website and databases of the National Organization for Rare Disorders NORD is copyrighted and kuver not be reproduced, copied, downloaded or disseminated, in any way, for any commercial or public purpose, without prior written authorization and approval from NORD.

Adjustment disorder with depressed mood. This may be the result of trauma to the brain itself, or the result of other degenerative brain diseases, tumors, or it can be caused by some brain infections, most commonly herpes simplex encephalitis a viral brain infection.

Comparisons may be useful for a differential diagnosis: As memory losses increase, personality, mood and behavior also tend to change.

First aired September 12, All studies receiving U. Social neurosciences research shows that changes in temporal lobe is identified as a cause for aberrant sexual and hyper-sexual behaviors. Adult personality and behavior Gender dysphoria Sexual maturation disorder Ego-dystonic sexual bkcy Sexual relationship disorder Paraphilia Voyeurism Fetishism.


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KBS is now thought to be caused by disturbances of temporal portions of limbic networks that interface with multiple cortical and subcortical circuits to modulate emotional behavior and affect. The Kluver-Bucy syndrome is a clinical syndrome observed in humans and other animals after bilateral lesions in the temporal lobe that involve the amygdala, hippocampal formation, and adjacent neural structures. Disorders typically diagnosed in childhood. Various attempts were made to localize the component features to specific areas of the temporal lobe, with mixed success.

Bergman; Ronald Arly Bergman Some current clinical trials also are posted on the following page on the NORD website: Bilateral ventral temporal ablations and bilateral temporal lobectomies produced marked impairment in visual discrimination, whereas lateral resections or unilateral lesions did not. Memories Are Made of This: Personality disorder Impulse lkuver disorder Kleptomania Trichotillomania Pyromania Dermatillomania Factitious disorder Munchausen syndrome.

Human cases were recognized in the s, as surgeons employed bilateral temporal lobectomies to treat seizures. Frontotemporal degeneration is a very rare progressive neurological disease synvrome predominately affecting the frontal and temporal lobes of the brain. An almost uncontrollable appetite for food may also be noted.

Mental disorders due to a general medical condition Sexual arousal Syndromes affecting the nervous system Amygdala Psychopathological syndromes Rare syndromes. Alzheimer disease is a common progressive disorder of the brain affecting memory, thought and language.


Postpartum depression Postpartum psychosis. Produced by Jad Abumrad.

Principles of Neurology, 6th ed. Korsakoff syndrome is a deficiency of vitamin B-1 that leads to cardiovascular, central and peripheral nervous system disturbances. Box Bethesda, MD Phone: However, in later stages there is loss of motor control as well as confusion and severe dementia. Sapolsky, who addresses the syndrome and the associated legal significance of neurological defenses. Judgment, synerome, speech and physical coordination may also be affected. The treatment of KBS is difficult and often unsatisfactory.

Kluver-Bucy Syndrome – Temporal Lobectomy Behavior Syndrome – information page with HONselect

Dissociative identity disorder Psychogenic amnesia Fugue state Depersonalization disorder. Disorganized hebephrenic schizophrenia Paranoid schizophrenia Simple-type schizophrenia Childhood schizophrenia Pseudoneurotic schizophrenia.

The Neuropsychiatry of Limbic and Subcortical Disorders. How Memory Works in Humans and Animals. D ICD – Views Read Edit View history.

Klüver-Bucy Syndrome Information Page

Government funding, and some supported by private industry, are posted on this government web site. Retrieved from ” https: Neuroticstress -related and somatoform Anxiety disorder Phobia Agoraphobia Social anxiety Social phobia Anthropophobia Specific social phobia Specific phobia Claustrophobia. Infobox medical condition new.

Accessed March 19, There may also be other symptoms associated with dementia loss of reason as well. Sexual maturation disorder Ego-dystonic sexual orientation Sexual relationship disorder Paraphilia Voyeurism Fetishism.

For information about clinical trials conducted in Europe, contact: